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Anesthetic Management of a Boy with Congenital Disorder of Glycosylation (CDG) I-x
Department of Anesthesiology
- 1 Department of Anesthesiology
- 2
- 3
International Journal of Clinical Medicine·Volume 02 (2011)·Pages 325–327·Published 13 July 2011·DOI10.4236/ijcm.2011.23056
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Abstract
Congenital disorders of glycosylation (CDGs) are group group of genetic defects in the assembly and processing pathway of protein glycosylation, which cause a wide range of multi system dysfunction. This paper describes the anesthetic management of 6 year old boy with CDG type I-x for upper airway surgery. We used a sevoflurane-nitrous oxide-remifentanil regime with no complications and good results. As for now, the literature lacks reports of anesthetic management of children with CDG I-x, and this report may provide clinicians an option for safe anesthetic management.
KeywordsAnesthesiaPediatricMetabolic DisordersCongenital Disorders of GlycosylationCDG
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