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Case Report of Prosthetic Treatment of a Young Patient Suffering Papilon-Lefever Syndrome
Department of Prosthodontics, Faculty of Dentistry, Kurdistan University of Medical Science, Sanandaj, Iran
Department of Prosthodontics, Faculty of Dentistry, Tehran University of Medical Science, Tehran, Iran
Department of Endodontics, Faculty of Dentistry, Kurdistan University of Medical Science, Sanandaj, Ira
- 1 Department of Prosthodontics, Faculty of Dentistry, Kurdistan University of Medical Science, Sanandaj, Iran
- 2 Department of Prosthodontics, Faculty of Dentistry, Tehran University of Medical Science, Tehran, Iran
- 3 Department of Endodontics, Faculty of Dentistry, Kurdistan University of Medical Science, Sanandaj, Ira
International Journal of Clinical Medicine·Volume 08 (2017)·Pages 422–429·Published 16 June 2017·DOI10.4236/ijcm.2017.86040
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Abstract
Papillon-Lefevre syndrome (PLS) is a rare recessive autosomal disease which occurs with palms and soles hyperkeratosis as well as primary and permanent teeth periodontal loss. Recently, it has been proved that a mutation at Cathepsin gene C is the genetic cause of PLS. All primary and permanent teeth of the patients are lost at ages 2 or 3 because of serious alveolar bone destruction. This paper presents a complete case of prosthetic treatment of an 8-year old girl with PLS.
KeywordsProsthetic TreatmentYoung PatientPapilon-Lefever Syndrome
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