Primary Synovial Sarcoma of the Kidney: A Case Report
- 1 Medical Onocology Department, University Hospital Farhat Hached, Sousse, Tunisia
- 2 Medical Onocology Department, University Hospital Farhat Hached, Sousse, Tunisia
- 3 Medical Onocology Department, University Hospital Farhat Hached, Sousse, Tunisia
- 4 Medical Onocology Department, University Hospital Farhat Hached, Sousse, Tunisia
- 5 Medical Onocology Department, University Hospital Farhat Hached, Sousse, Tunisia
- 6 Medical Onocology Department, University Hospital Farhat Hached, Sousse, Tunisia
- 7 Pediatric Surgery Department, University Hospital Fatouma Bourguiba, Monastir, Tunisia
- 8 Medical Onocology Department, University Hospital Farhat Hached, Sousse, Tunisia
- 9 Medical Onocology Department, University Hospital Farhat Hached, Sousse, Tunisia
- 10 Anathomopathology Department, University Hospital Fatouma Bourguiba, Monastir, Tunisia
- 11 Radiotherapy Department, University Hospital Farhat Hached, Sousse, Tunisia
- 12 Pediatric Surgery Department, University Hospital Fatouma Bourguiba, Monastir, Tunisia
- 13 Radiology Department, University Hospital Fatouma Bourguiba, Monastir, Tunisia
- 14 Anathomopathology Department, University Hospital Fatouma Bourguiba, Monastir, Tunisia
- 15 Medical Onocology Department, University Hospital Farhat Hached, Sousse, Tunisia
Abstract
Synovial sarcoma originating from the kidney is extremely rare. A 13-year-old girl presented with a mild left flank pain of one-week duration, with no associated history of hematuria or any other systemic symptoms. Computed tomography (CT) demonstrated a 6 × 13 × 9 cm mass in the left kidney. No soft tissue or extrarenal masses were identified. The patient received a combined of treatment with doxorubicin and ifosfamide. A radical nephrectomy was performed in the left kidney with no complications. Postoperative pathology revealed post-chemotherapy residue of monophasic spindle cell synovialosarcoma of the left kidney. She received a combined treatment with doxorubicin and ifosfamide in concomittance with external radiation therapy. The patient was re-examined 4 months after surgery. An abdominal and pulmonary CT found no recurrence or metastasis.
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