Huge Sacrococcygeal Teratoma in an Adult Female: A Case Report
- 1 Department of Surgery, Fuchu Hospital, Izumi, Osaka, Japan
- 2 Department of Surgery, Fuchu Hospital, Izumi, Osaka, Japan
- 3 Department of Surgery, Fuchu Hospital, Izumi, Osaka, Japan
- 4 Department of Surgery, Fuchu Hospital, Izumi, Osaka, Japan
- 5 Department of Surgery, Fuchu Hospital, Izumi, Osaka, Japan
- 6 Department of Surgery, Fuchu Hospital, Izumi, Osaka, Japan
- 7 Department of Surgery, Fuchu Hospital, Izumi, Osaka, Japan
- 8 Department of Surgery, Fuchu Hospital, Izumi, Osaka, Japan
- 9 Department of Surgery, Fuchu Hospital, Izumi, Osaka, Japan
- 10 Department of Surgery, Fuchu Hospital, Izumi, Osaka, Japan
Abstract
Background: Teratomas are a type of germ cell tumor, which are mostly benign, and dominative in adult females. Sacococcygeal teratomas are usually found in newborns or children, and can be detected prenatally; they are exceedingly rare in adults. We reported a case of a sacrococcygeal teratoma in adult female. Case presentation: A 26-year-old female was diagnosed with a presacral tumor 6 years ago. Pelvic computed tomography (CT) demonstrated a presacral heterogeneous tumor, containing multi - located cystic area and enhanced solid component with calcification. Magnetic resonance imaging (MRI) showed a presacral non-enhanced cystic lesion with solid component, 128 mm × 104 mm × 102 mm, which was suspected of having invaded the rectal wall, fi fth sacral vertebra (S5), and coccyx. She underwent abdomino-sacral total excision of tumor with coccygectomy. Histopathological examination revealed a tumor with intricate admixture of ectodermal (epidermis, sebaceous glands and squamous), mesenchymal (cartilage, adipose tissue, blood vessels, nerves and skeletal muscle) and endodermal components (respiratory epithelium and intestinal epithelium) respectively. A fter 24 months of follow - up the patient was both clinically and radiologically disease free. Conclusions: Early complete excision was the preferred definitive modality of treatment for sacrococcygeal teratoma, and multi-staged excision and reconstruction resulted in successful and safe treatment in our case.
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