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Comparative Analysis of Post-Rehabilitation Neuropsychological Profile of a Patient with Susac Syndrome—A Case Report
Hospital Universitario de la Samaritana, Bogotá, Colombia
Hospital Universitario de la Samaritana, Bogotá, Colombia
Hospital Universitario de la Samaritana, Bogotá, Colombia
Neuropsychological Assessment and Diagnosis Specialization Program, School of Psychology, Universidad San Buenaventura Bogotá, Bogotá, Colombia
Neuropsychological Assessment and Diagnosis Specialization Program, School of Psychology, Universidad San Buenaventura Bogotá, Bogotá, Colombia
Neuropsychological Assessment and Diagnosis Specialization Program, School of Psychology, Universidad San Buenaventura Bogotá, Bogotá, Colombia
Neuropsychological Assessment and Diagnosis Specialization Program, School of Psychology, Universidad San Buenaventura Bogotá, Bogotá, Colombia
Neuropsychological Assessment and Diagnosis Specialization Program, School of Psychology, Universidad San Buenaventura Bogotá, Bogotá, Colombia
Hospital Universitario de la Samaritana, Bogotá, Colombia
- 1 Hospital Universitario de la Samaritana, Bogotá, Colombia
- 2 Hospital Universitario de la Samaritana, Bogotá, Colombia
- 3 Hospital Universitario de la Samaritana, Bogotá, Colombia
- 4 Neuropsychological Assessment and Diagnosis Specialization Program, School of Psychology, Universidad San Buenaventura Bogotá, Bogotá, Colombia
- 5 Neuropsychological Assessment and Diagnosis Specialization Program, School of Psychology, Universidad San Buenaventura Bogotá, Bogotá, Colombia
- 6 Neuropsychological Assessment and Diagnosis Specialization Program, School of Psychology, Universidad San Buenaventura Bogotá, Bogotá, Colombia
- 7 Neuropsychological Assessment and Diagnosis Specialization Program, School of Psychology, Universidad San Buenaventura Bogotá, Bogotá, Colombia
- 8 Neuropsychological Assessment and Diagnosis Specialization Program, School of Psychology, Universidad San Buenaventura Bogotá, Bogotá, Colombia
- 9 Hospital Universitario de la Samaritana, Bogotá, Colombia
Neuroscience and Medicine·Volume 12 (2021)·Pages 79–89·Published 23 September 2021·DOI10.4236/nm.2021.123007
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Abstract
Susac Syndrome (SS) is an autoimmune disease characterized by the clinical triad of encephalopathy, hearing loss and retinal arterial occlusions, with prevalent structural changes identified on brain magnetic resonance imaging (white matter, corpus callosum, basal ganglia region and the thalamic region extending to the midbrain) in the majority of cases, which lead to cognitive manifestations of which there is a paucity of descriptions in the literature. The objective of this case study is to compare to post-rehabilitation neurocognitive profile of a 29-year-old woman with SS presenting with compromised intellectual and motor skills and cognitive functions, together with neuropsychiatric symptoms. Better performance was found in the neuropsychological assessment, with changes in the structural cerebral network evidenced on Diffusion Tensor Imaging (DTI) performed following the therapeutic and pharmacological intervention.
KeywordsSusac SyndromeDemyelinating DiseaseNeuropsychological AssessmentRehabilitation
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