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Advanced Imaging Techniques in Lhermitte-Duclos Disease (LDD): A Case Report and Brief Literature Review
Division of Radiology and Diagnostic Imaging, Universitary Hospital of the Federal University of Juiz de Fora, Juiz de Fora, Brazil
Division of Radiology and Diagnostic Imaging, Universitary Hospital of the Federal University of Juiz de Fora, Juiz de Fora, Brazil
Division of Radiology and Diagnostic Imaging, Universitary Hospital of the Federal University of Juiz de Fora, Juiz de Fora, Brazil
Division of Radiology and Diagnostic Imaging, Universitary Hospital of the Federal University of Juiz de Fora, Juiz de Fora, Brazil
Division of Radiology and Diagnostic Imaging, Universitary Hospital of the Federal University of Juiz de Fora, Juiz de Fora, Brazil
Division of Radiology and Diagnostic Imaging, Universitary Hospital of the Federal University of Juiz de Fora, Juiz de Fora, Brazil
Division of Radiology and Diagnostic Imaging, Universitary Hospital of the Federal University of Juiz de Fora, Juiz de Fora, Brazil
- 1 Division of Radiology and Diagnostic Imaging, Universitary Hospital of the Federal University of Juiz de Fora, Juiz de Fora, Brazil
- 2 Division of Radiology and Diagnostic Imaging, Universitary Hospital of the Federal University of Juiz de Fora, Juiz de Fora, Brazil
- 3 Division of Radiology and Diagnostic Imaging, Universitary Hospital of the Federal University of Juiz de Fora, Juiz de Fora, Brazil
- 4 Division of Radiology and Diagnostic Imaging, Universitary Hospital of the Federal University of Juiz de Fora, Juiz de Fora, Brazil
- 5 Division of Radiology and Diagnostic Imaging, Universitary Hospital of the Federal University of Juiz de Fora, Juiz de Fora, Brazil
- 6 Division of Radiology and Diagnostic Imaging, Universitary Hospital of the Federal University of Juiz de Fora, Juiz de Fora, Brazil
- 7 Division of Radiology and Diagnostic Imaging, Universitary Hospital of the Federal University of Juiz de Fora, Juiz de Fora, Brazil
Neuroscience and Medicine·Volume 08 (2017)·Pages 1–7·Published 28 March 2017·DOI10.4236/nm.2017.81001
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Abstract
Lhermitte-Duclos disease (LDD), also called dysplastic gangliocytoma of the cerebellum, is a rare condition described in 1920. It represents a disorganization of cerebellar architecture with overgrowth of cerebellar ganglion cells which replace granular cells and Purkinje cells. In this report we present the case of a 62-year-old male affected by this disease, as well as literature review of the clinical, morphological and functional radiological findings.
KeywordsLhermitte-Duclos DiseaseDisplastic GangliocytomaCentral Nervous SystemMRI
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