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Caroli Disease: A Case Report Observed at the Cocody Teaching Hospital of Abidjan (Cote D’Ivoire)
Service D’Hépato-Gastro Entérologie CHU Cocody, Abidjan, Côte D’Ivoire
Service D’Hépato-Gastro Entérologie CHU Cocody, Abidjan, Côte D’Ivoire
Service D’Hépato-Gastro Entérologie CHU Cocody, Abidjan, Côte D’Ivoire
Service D’Hépato-Gastro Entérologie CHU Cocody, Abidjan, Côte D’Ivoire
Service D’Hépato-Gastro Entérologie CHU Cocody, Abidjan, Côte D’Ivoire
Service De Pédiatrie Médicale, CHU Cocody, Abidjan, Côte D’Ivoire
Service D’Imagerie Médicale, CHU Cocody, Abidjan, Côte D’Ivoire
Service D’Hépato-Gastro Entérologie CHU Cocody, Abidjan, Côte D’Ivoire
Service D’Hépato-Gastro Entérologie CHU Cocody, Abidjan, Côte D’Ivoire
Service D’Hépato-Gastro Entérologie CHU Cocody, Abidjan, Côte D’Ivoire
- 1 Service D’Hépato-Gastro Entérologie CHU Cocody, Abidjan, Côte D’Ivoire
- 2 Service D’Hépato-Gastro Entérologie CHU Cocody, Abidjan, Côte D’Ivoire
- 3 Service D’Hépato-Gastro Entérologie CHU Cocody, Abidjan, Côte D’Ivoire
- 4 Service D’Hépato-Gastro Entérologie CHU Cocody, Abidjan, Côte D’Ivoire
- 5 Service D’Hépato-Gastro Entérologie CHU Cocody, Abidjan, Côte D’Ivoire
- 6 Service De Pédiatrie Médicale, CHU Cocody, Abidjan, Côte D’Ivoire
- 7 Service D’Imagerie Médicale, CHU Cocody, Abidjan, Côte D’Ivoire
- 8 Service D’Hépato-Gastro Entérologie CHU Cocody, Abidjan, Côte D’Ivoire
- 9 Service D’Hépato-Gastro Entérologie CHU Cocody, Abidjan, Côte D’Ivoire
- 10 Service D’Hépato-Gastro Entérologie CHU Cocody, Abidjan, Côte D’Ivoire
Open Journal of Gastroenterology·Volume 07 (2017)·Pages 28–31·Published 6 January 2017·DOI10.4236/ojgas.2017.71004
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Abstract
Caroli disease is a rare affection. It’s commonly associated to polycystic kidneys. We report a case of a nine-year-old girl. She was hospitalized at the pediatric unit of the Cocody Teaching Hospital for an intermittent fever. During the clinical examination, we found a likely cirrhotic hepatomegaly associated to an edematous-ascitic syndrome. Biological exams showed an infectious syndrome with a hyperleukocytosis at 13.000 per mm 3 , a hyperneutrophilia at 9.600 per mm 3 . Serological viral markers of B, C and D hepatitis were negative. We saw an intra-hepatic cystic picture at the liver CT-scan with a vascular lesion at his center called a “dot sign”. The diagnosis of Caroli disease could be evocated.
KeywordsCarolisyndromCongenital Cystic DilationCholangitisLiver CT-Scan
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