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Adult Langerhans Cell Histiocytosis: A Rare Etiology of Spinal Cord Compression
Department of Radiotherapy, National Institute of Oncology, Rabat, Morocco
Department of Radiotherapy, National Institute of Oncology, Rabat, Morocco
Department of Radiotherapy, National Institute of Oncology, Rabat, Morocco
Department of Radiotherapy, National Institute of Oncology, Rabat, Morocco
Department of Pathology, National Institute of Oncology, Rabat, Morocco
Department of Pathology, National Institute of Oncology, Rabat, Morocco
Department of Medical Oncology, National Institute of Oncology, Rabat, Morocco
Department of Medical Oncology, National Institute of Oncology, Rabat, Morocco
Department of Radiology, National Institute of Oncology, Rabat, Morocco
Department of Radiotherapy, National Institute of Oncology, Rabat, Morocco
Department of Radiotherapy, National Institute of Oncology, Rabat, Morocco
Department of Radiotherapy, National Institute of Oncology, Rabat, Morocco
Department of Radiotherapy, National Institute of Oncology, Rabat, Morocco
- 1 Department of Radiotherapy, National Institute of Oncology, Rabat, Morocco
- 2 Department of Radiotherapy, National Institute of Oncology, Rabat, Morocco
- 3 Department of Radiotherapy, National Institute of Oncology, Rabat, Morocco
- 4 Department of Radiotherapy, National Institute of Oncology, Rabat, Morocco
- 5 Department of Pathology, National Institute of Oncology, Rabat, Morocco
- 6 Department of Pathology, National Institute of Oncology, Rabat, Morocco
- 7 Department of Medical Oncology, National Institute of Oncology, Rabat, Morocco
- 8 Department of Medical Oncology, National Institute of Oncology, Rabat, Morocco
- 9 Department of Radiology, National Institute of Oncology, Rabat, Morocco
- 10 Department of Radiotherapy, National Institute of Oncology, Rabat, Morocco
- 11 Department of Radiotherapy, National Institute of Oncology, Rabat, Morocco
- 12 Department of Radiotherapy, National Institute of Oncology, Rabat, Morocco
- 13 Department of Radiotherapy, National Institute of Oncology, Rabat, Morocco
Open Journal of Internal Medicine·Volume 05 (2015)·Pages 21–28·Published 20 August 2015·DOI10.4236/ojim.2015.53005
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Abstract
Langerhans cell histiocytosis is a rare disease involving clonal proliferation of langerhans cells seen in children and young adults. Clinical presentation is variable, ranging from a single location in the bone to severe multivisceral involvement. Moreover, spinal involvement causing myelopathy is even rare and unusual. We report a rare case of adult Langerhans cell histiocytosis in the dorsal spine causing a spinal cord compression associated with a pulmonary process treated by surgery, radiotherapy and systemic therapy with good evolution.
KeywordsLangerhans Cell HistiocytosisAdultsSpinal Cord Compression
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