Giant Angiomyolipoma of the Kidney Presenting as Anaemia—A Rare Presentation
- 1 Department of Surgery, Maulana Azad Medical College and Lok Nayak Hospital, New Delhi, India
- 2 Department of Surgery, Maulana Azad Medical College and Lok Nayak Hospital, New Delhi, India
- 3 Department of Surgery, Maulana Azad Medical College and Lok Nayak Hospital, New Delhi, India
- 4 Department of Surgery, Maulana Azad Medical College and Lok Nayak Hospital, New Delhi, India
Abstract
Angiomyolipoma presenting with severe anaemia is a rare entity. Urgent operative intervention is warranted in such patients especially if the tumour is “Giant” i.e. greater than 10 cm and involves the whole kidney. We chronicle the case of a 35 year old lady who presented with a rapidly enlarging renal lump in the left loin associated with severe anaemia. MRI was highly suggestive of angiomyolipoma. She underwent nephrectomy in view of continuous intratumoral haemorrhage. The tumour measured 18 × 13 × 8 cm and weighed approximately 1.6 kilograms after removing blood and blood clots. The histopathology was suggestive of angiomyolipoma. Angioembolization may be considered for tumours involving a portion of the kidney, as a part of the nephron sparing approach.
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