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A Rare Cause of Melaena-Duodenal Gangliocytic Paraganglioma
Department of Surgery, Lyell McEwin Hospital, Elizabeth Vale, Australia
Department of Surgery, Lyell McEwin Hospital, Elizabeth Vale, Australia
Department of Surgery, Lyell McEwin Hospital, Elizabeth Vale, Australia
Department of Surgery, Lyell McEwin Hospital, Elizabeth Vale, Australia
- 1 Department of Surgery, Lyell McEwin Hospital, Elizabeth Vale, Australia
- 2 Department of Surgery, Lyell McEwin Hospital, Elizabeth Vale, Australia
- 3 Department of Surgery, Lyell McEwin Hospital, Elizabeth Vale, Australia
- 4 Department of Surgery, Lyell McEwin Hospital, Elizabeth Vale, Australia
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Abstract
Gangliocytic paraganglioma (GP), a rare tumour that arises most frequently from the periampullary area, is considered to be a benign neoplasm with a potential for lymphatic spread. Distant metastases are rare [1]. We report a case of a 51 year old female who presented with abdominal pain, anaemia and melaena. Endoscopy, push enteroscopy and biopsy revealed a periampullary neuroendocrine tumour. Immunohistochemistry of the pancreatic duodenectomy specimen demonstrated a duodenal gangliocytic paraganglioma with no lymph node metastases. We review the literature on this rare tumour and the current treatment protocol.
KeywordsMelaenaRare TumourNeuroendocrine TumourDiagnostic Histological TriadGangliocytic Paraganglioma
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